Sjögren’s syndrome: state of the art on clinical practice guidelines
Vasco Romão
(1)
,
Rosaria Talarico
(2)
,
Carlo Alberto Scirè
(3)
,
Ana Vieira
(4)
,
Tobias Alexander
(5)
,
Chiara Baldini
(2, 6)
,
Jacques-Eric Gottenberg
(7, 8)
,
Heidi Gruner
(9)
,
Eric Hachulla
(10, 11)
,
Luc Mouthon
(12, 13)
,
Martina Orlandi
(14)
,
Cristina Pamfil
,
Marc Pineton de Chambrun
(15, 16)
,
Marco Taglietti
(17)
,
Natasa Toplak
(18)
,
Paul van Daele
(19)
,
Jacob van Laar
(20)
,
Stefano Bombardieri
(6)
,
Matthias Schneider
(21)
,
Vanessa Smith
(22)
,
Maurizio Cutolo
(23)
,
Marta Mosca
(6, 2)
,
Xavier Mariette
(24, 25)
1
CHULN -
Centro Hospitalar Universitário Lisboa Norte [Lisbon, Portugal]
2 Azienda Ospedaliera Universitaria Pisana
3 UniFE - Università degli Studi di Ferrara = University of Ferrara
4 LPCDR - Liga Portuguesa Contra as Doenças Reumaticas
5 Charité - UniversitätsMedizin = Berlin University Medicine
6 UniPi - University of Pisa [Italy] = Università di Pisa [Italia] = Université de Pise [Italie]
7 IRM - Immuno-Rhumatologie Moléculaire
8 HUS - Les Hôpitaux Universitaires de Strasbourg
9 Centro Hospitalar de Lisboa Central E.P.E
10 INFINITE - Institute for Translational Research in Inflammation - U 1286
11 CHRU Lille - Centre Hospitalier Régional Universitaire [CHU Lille]
12 Hôpital Cochin [AP-HP]
13 UPD5 - Université Paris Descartes - Paris 5
14 UniFI - Università degli Studi di Firenze = University of Florence = Université de Florence
15 CHU Pitié-Salpêtrière [AP-HP]
16 SU - Sorbonne Université
17 Azienda Socio Sanitaria Territoriale Spedali Civili di Brescia [Brescia]
18 UMCL - University Medical Centre Ljubljana [Ljubljana, Slovenia]
19 Erasmus MC - Erasmus University Medical Center [Rotterdam]
20 Universiteit Utrecht / Utrecht University [Utrecht]
21 University Hospital Düsseldorf
22 Ghent University Hospital
23 UniGe - Università degli studi di Genova = University of Genoa
24 IMVA - U1184 - Immunologie des Maladies Virales et Autoimmunes
25 HUPS - Hôpitaux Universitaires Paris Sud [AP-HP]
2 Azienda Ospedaliera Universitaria Pisana
3 UniFE - Università degli Studi di Ferrara = University of Ferrara
4 LPCDR - Liga Portuguesa Contra as Doenças Reumaticas
5 Charité - UniversitätsMedizin = Berlin University Medicine
6 UniPi - University of Pisa [Italy] = Università di Pisa [Italia] = Université de Pise [Italie]
7 IRM - Immuno-Rhumatologie Moléculaire
8 HUS - Les Hôpitaux Universitaires de Strasbourg
9 Centro Hospitalar de Lisboa Central E.P.E
10 INFINITE - Institute for Translational Research in Inflammation - U 1286
11 CHRU Lille - Centre Hospitalier Régional Universitaire [CHU Lille]
12 Hôpital Cochin [AP-HP]
13 UPD5 - Université Paris Descartes - Paris 5
14 UniFI - Università degli Studi di Firenze = University of Florence = Université de Florence
15 CHU Pitié-Salpêtrière [AP-HP]
16 SU - Sorbonne Université
17 Azienda Socio Sanitaria Territoriale Spedali Civili di Brescia [Brescia]
18 UMCL - University Medical Centre Ljubljana [Ljubljana, Slovenia]
19 Erasmus MC - Erasmus University Medical Center [Rotterdam]
20 Universiteit Utrecht / Utrecht University [Utrecht]
21 University Hospital Düsseldorf
22 Ghent University Hospital
23 UniGe - Università degli studi di Genova = University of Genoa
24 IMVA - U1184 - Immunologie des Maladies Virales et Autoimmunes
25 HUPS - Hôpitaux Universitaires Paris Sud [AP-HP]
Carlo Alberto Scirè
- Fonction : Auteur
- PersonId : 808159
- ORCID : 0000-0001-7451-0271
Tobias Alexander
- Fonction : Auteur
- PersonId : 1248566
- ORCID : 0000-0003-1193-0097
Luc Mouthon
- Fonction : Auteur
- PersonId : 1330915
- ORCID : 0000-0002-9838-246X
- IdRef : 069140634
Cristina Pamfil
- Fonction : Auteur
Résumé
Sjögren’s syndrome (SS) is a complex autoimmune rheumatic disease that specifically targets salivary and lachrymal glands. As such, patients typically had ocular and oral dryness and salivary gland swelling. Moreover, skin, nasal and vaginal dryness are frequently present. In addition to dryness, musculoskeletal pain and fatigue are the hallmarks of this disease and constitute the classic symptom triad presented by the vast majority of patients. Up to 30% to 50 % of patients with SS may present systemic disease; moreover, there is an increased risk for the development of non-Hodgkin’s lymphoma that occurs in a minority of patients. The present work was developed in the framework of the European Reference Network (ERN) dedicated to Rare and Complex Connective Tissue and Musculoskeletal Diseases (ReCONNET). In line with its goals of aiming to improve early diagnosis, treatment and care of rare connective and musculoskeletal diseases, ERN-ReCONNET set to review the current state of clinical practice guidelines (CPGs) in the rare and complex connective tissue diseases of interest of the network. Therefore, the present work was aimed at providing a state of the art of CPGs for SS.