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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Regenerative medicine
Muscular dystrophy
Myogenesis
Haploinsufficiency
Muscle dystrophy
Neuromuscular junction NMJ
Regulatory T cells
Dystrophie musculaire oculopharyngée
Intercellular communication
Actin
Akt
Dystrophin
Triplet expansion disease
Nuclear envelope
Ageing
2-D PAGE
Amyotrophic Lateral Sclerosis
Fibrosis
ARN
AAV vectors
RNA
Myoblast
Anti-acetylcholine receptor antibodies
Transcriptomics
Duchenne muscular dystrophy
Human
APOPTOSIS
Xenograft
Autologous
Myoblasts
Antiserum
AUTOPHAGY
Muscle
Satellite cell
Muscle strength
Annexin A2
Cross-bridge kinetics
Inflammation
Cell therapy
Calcium
Biomarker
Dysferlinopathy
Satellite cells
BINDING SPECIFICITY
Geriatric assessment
Metabolism
FAPs
Myosin
PABPN1
Myopathy
Muscle fibrosis
Alphavirus
Skeletal muscle
Effector T cells
Differentiation
Pharyngeal muscle
Myotube
GENE
Agrégats de PABPN1
Aav-U7
DUX4
Mass spectrometry
Atrophy
Accelerometry
Alzheimer's disease
AChR antibodies
Anti-fibrotic pharmacotherapies
Autoimmune diseases
Omics
DNA methylation
Arbovirus
Lamins
Bile salt hydrolases
Adipose tissue
OPMD
AAV
Gene replacement
Muscle stem cells
Oculopharyngeal muscular dystrophy
Regeneration
Aggregate
MUTATIONS
Epigenetics
Exon-skipping
Antisens oligonucleotides
Myopathies
Aged
Functional genomics
Gene therapy
Pax7
Sarcopenia
ALS
DMD
Thérapie génique
Andermann syndrome
Dysferlin
Neuromuscular disease
Myositis
FSHD
PABPN1 agregates