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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Triplet expansion disease
Lamins
Aged
Regenerative medicine
Muscle stem cells
Muscle dystrophy
Pharyngeal muscle
Cell therapy
Metabolism
AChR antibodies
Dystrophin
Bile salt hydrolases
Mass spectrometry
FSHD
Transcriptomics
BINDING SPECIFICITY
FAPs
Intercellular communication
RNA
Thérapie génique
Atrophy
Myopathies
Functional genomics
PABPN1 agregates
Myoblast
2-D PAGE
Effector T cells
Muscle strength
Alphavirus
GENE
Autoimmune diseases
Myositis
Exon-skipping
Cross-bridge kinetics
Dysferlinopathy
Accelerometry
Epigenetics
PABPN1
Antisens oligonucleotides
Oculopharyngeal muscular dystrophy
Annexin A2
Calcium
Aggregate
Antiserum
Gene therapy
Gene replacement
Myotube
Human
Actin
OPMD
Adipose tissue
Myogenesis
Amyotrophic Lateral Sclerosis
Aav-U7
Inflammation
ALS
Muscular dystrophy
AAV vectors
Geriatric assessment
Regulatory T cells
Regeneration
Akt
MUTATIONS
Dystrophie musculaire oculopharyngée
Skeletal muscle
Myoblasts
Satellite cells
Anti-fibrotic pharmacotherapies
DMD
DUX4
Myopathy
Haploinsufficiency
Nuclear envelope
ARN
Agrégats de PABPN1
Neuromuscular junction NMJ
Anti-acetylcholine receptor antibodies
Sarcopenia
Andermann syndrome
Alzheimer's disease
Differentiation
Neuromuscular disease
Autologous
DNA methylation
APOPTOSIS
Xenograft
Arbovirus
Satellite cell
Omics
AAV
AUTOPHAGY
Dysferlin
Duchenne muscular dystrophy
Ageing
Myosin
Biomarker
Muscle
Fibrosis
Pax7
Muscle fibrosis